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G71.0349 ICD-10-CM Code: Limb girdle muscular dystrophy due to other sarcoglycan dysfunction

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FY 2026 Apr update / Diseases of the nervous system (G00-G99) / Diseases of myoneural junction and muscle (G70-G73)

G71.0349

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Limb girdle muscular dystrophy due to other sarcoglycan dysfunction

A genetic muscle weakness disorder affecting the hip and shoulder muscles caused by dysfunction of sarcoglycan proteins other than alpha or beta subtypes.

Buddy the Bee presenting code insight

Buddy Insight

Limb girdle muscular dystrophy due to other sarcoglycan dysfunction captures gamma-sarcoglycan (LGMD2C), delta-sarcoglycan (LGMD2F), and epsilon-sarcoglycan deficiencies.

CMS-HCC V28

HCC 197

RAF 0.0

CMS-HCC V24

HCC 76

RAF 0.358

ACA/HHS

0

0

RAF 0

ESRD/PACE

HCC 76

RAF 0.0

RXHCC

0

0

RAF 0

Code Trumping

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Code Book Path

Official
G71.03Limb girdle muscular dystrophies
G71.034Limb girdle muscular dystrophy due to sarcoglycan dysfunction
G71.0349Limb girdle muscular dystrophy due to other sarcoglycan dysfunction

Inclusion Terms

Official
  • Delta sarcoglycanopathy
  • Delta-sarcoglycan-related LGMD R6
  • Gamma sarcoglycanopathy
  • Gamma-sarcoglycan-related LGMD R5
  • Limb girdle muscular dystrophy type 2C

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for G71.0349 in this effective period.

Related Child Codes

Official
G71.0340Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified
G71.0341Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
G71.0342Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction

Includes

Official

ICD-10-CM does not list Includes notes for G71.0349 in this effective period.

Excludes 1

Official

ICD-10-CM does not list Excludes 1 notes for G71.0349 in this effective period.

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for G71.0349 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for G71.0349 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for G71.0349 in this effective period.

Buddy Documentation Tip

HCC Buddy guidance
Genetic testing identifying the specific sarcoglycan mutation (gamma, delta, or epsilon)
Muscle biopsy showing specific sarcoglycan protein deficiency when available
Clinical presentation: severity, distribution of weakness, age of onset
Cardiac and respiratory function assessments

MEAT Support

HCC Buddy guidance
Genetic testing identifying the specific sarcoglycan mutation (gamma, delta, or epsilon)
Muscle biopsy showing specific sarcoglycan protein deficiency when available
Clinical presentation: severity, distribution of weakness, age of onset
Cardiac and respiratory function assessments

Audit Caution

HCC Buddy guidance
Defaulting to the unspecified sarcoglycan code when genetic testing has identified gamma, delta, or epsilon involvement
Using this code for alpha or beta sarcoglycanopathy, which have their own specific codes
Not documenting which specific sarcoglycan subtype is affected in the medical record
Failing to code cardiac and respiratory complications separately when present

Common Mistakes

HCC Buddy guidance
G71.0340 — Sarcoglycan dysfunction, unspecified is for when the subtype is completely unknown
G71.0341 — Alpha sarcoglycan dysfunction has its own specific code
G71.0342 — Beta sarcoglycan dysfunction has its own specific code
G71.038 — Other limb girdle muscular dystrophy is for non-sarcoglycan-related limb girdle dystrophies

Last updated: FY2026 ICD-10-CM Apr update, Apr 1, 2026 through Sep 30, 2026. CMS-HCC V28 is 100% phased in for payment year 2026.

Is G71.0349 an HCC code?

Yes. G71.0349 maps to Muscular Dystrophy under the CMS-HCC V28 risk adjustment model (and Muscular Dystrophy under V24).

HCC Category Mapping

V28HCC 197, Muscular Dystrophy
0.000
V24HCC 76, Muscular Dystrophy
0.358
ESRDHCC 76, Muscular Dystrophy
0.000

RAF weights shown are the community, non-dual, aged base weights from the CMS risk adjustment model file. Actual per-patient RAF contribution depends on member segment, interactions, and the model year used by the payer. V28 is the CMS-HCC model phased in over payment years 2024–2026; V24 remains in use during the transition and for historical data.

MEAT Criteria for G71.0349

For G71.0349to count as a valid HCC diagnosis in a given encounter, the provider's documentation must show MEAT: Monitor, Evaluate, Assess, or Treat. A diagnosis from a prior year does not carry forward automatically, it has to be re-documented and supported each calendar year.

  • MMonitor: signs, symptoms, disease progression, or lab trending documented in the note
  • EEvaluate: test results, medication response, or physical findings reviewed by the provider
  • AAssess: explicit mention in the assessment or plan with acknowledgment of status
  • TTreat: medication, referral, procedure, therapy, or counseling tied to the diagnosis

Only one of M/E/A/T is required to support the code, but the documentation must be specific enough to show that the provider actually addressed G71.0349 during that encounter, not just copy-forwarded from a problem list.

What This Code Means

G71.0349 is the ICD-10-CM diagnosis code for limb girdle muscular dystrophy due to other sarcoglycan dysfunction. A genetic muscle weakness disorder affecting the hip and shoulder muscles caused by dysfunction of sarcoglycan proteins other than alpha or beta subtypes. G71.0349 sits in the ICD-10-CM chapter for diseases of the nervous system (g00-g99), within the section covering diseases of myoneural junction and muscle (g70-g73).

Under the CMS-HCC V28 risk adjustment model, G71.0349 maps to Muscular Dystrophy (HCC 197) with a community, non-dual, aged base RAF weight of 0.000. Under the older V24 model, G71.0349 mapped to the same category but with a base RAF weight of 0.358, V28 recalibrated weights across the entire model. V28 is the CMS-HCC risk adjustment model that reached 100% phase-in for payment year 2026, replacing V24 which was used during the PY2024–PY2025 transition.

Use this code for gamma, delta, or epsilon sarcoglycan dysfunction when specifically identified. Because G71.0349 maps to a payment HCC, the provider's documentation must satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) for the encounter to count toward the patient's Medicare Advantage risk adjustment score. When documentation is ambiguous, coders should issue a provider query rather than assume the highest-specificity variant.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for G71.0349 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

  • Use this code for gamma, delta, or epsilon sarcoglycan dysfunction when specifically identified
  • Document which sarcoglycan subtype is affected in the medical record for clarity

Clinical Significance

Limb girdle muscular dystrophy due to other sarcoglycan dysfunction captures gamma-sarcoglycan (LGMD2C), delta-sarcoglycan (LGMD2F), and epsilon-sarcoglycan deficiencies. These rarer sarcoglycanopathies have variable severity but can be as severe as Duchenne muscular dystrophy. Precise identification of the sarcoglycan subtype is important for genetic counseling and emerging gene therapy approaches.

Documentation Requirements

  • Genetic testing identifying the specific sarcoglycan mutation (gamma, delta, or epsilon)
  • Muscle biopsy showing specific sarcoglycan protein deficiency when available
  • Clinical presentation: severity, distribution of weakness, age of onset
  • Cardiac and respiratory function assessments
  • Documentation specifying which sarcoglycan subtype (other than alpha or beta) is affected
  • Family history and inheritance pattern documentation

Commonly Confused Codes

  • G71.0340 — Sarcoglycan dysfunction, unspecified is for when the subtype is completely unknown
  • G71.0341 — Alpha sarcoglycan dysfunction has its own specific code
  • G71.0342 — Beta sarcoglycan dysfunction has its own specific code
  • G71.038 — Other limb girdle muscular dystrophy is for non-sarcoglycan-related limb girdle dystrophies

Child Codes

Code Hierarchy

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